ICD-10-CM Code for MERRF syndrome E88.42

ICD-10 code E88.42 for MERRF syndrome is a medical classification as listed by WHO under the range - Endocrine, nutritional and metabolic diseases .

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MERRF syndrome
Myoclonic epilepsy associated with ragged-red fibers
Code also progressive myoclonic epilepsy (G40.3-)


Excludes1: disorders of pyruvate metabolism (E74.4)
Kearns-Sayre syndrome (H49.81)
Leber's disease (H47.22)
Leigh's encephalopathy (G31.82)
Mitochondrial myopathy, NEC (G71.3)
Reye's syndrome (G93.7)


Excludes1: histiocytosis X (chronic) (C96.6)

Use additional codes for associated conditions

Get crucial instructions for accurate ICD-10-CM E88.42 coding with all applicable Excludes 1 and Excludes 2 notes from the section level conveniently shown with each code.
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